Bilateral Adrenalectomy in a 15 Year Old Patient with Adrenal Pheochromocytoma
DOI:
https://doi.org/10.54212/27068048.v11i2.146Keywords:
Pheochromocytoma , Bilateral adrenalectomyAbstract
Objective: To report a case of open bilateral adrenalectomy in a patient with pheochromocytoma. Presentation of clinical case: 15 year old female consulted for five months of sweating and palpitations. At medical evaluation hypertension, diaphoresis and visual disturbances were documented and therefore complementary studies were performed; abdominal tomography revealed a bilateral adrenal tumor stage T2, N0, M0. Bilateral open adrenalectomy was de decided treatment. After surgery, patient is transferred to an Intensive Care Unit presenting adequate evolution. After one week of hospitalization patient is discharged with steroid use and plan of ambulatory following in six weeks. In the follow up histopathology confirmed the presence of pheochromocytoma confined to the adrenal glands, without capsular extension and without lymphovascular invasion. Discussion: Neuroendocrine tumors as pheochromocytomas are infrequent malignant growths originated in enterochromaffin adrenal cells that cause sympathomimetic syndromes. Initial treatment consists in pharmacological blockade and definitive treatment is complete resection of the tumor. Laparoscopic adrenalectomy is the surgical treatment of choice in most patients. Open adrenalectomy is indicated in patients with tumors >6-8cm, with complex localization or when there are other compromised organs. Conclusion: Pheochromocytomas are infrequent and silent adrenal tumors; definitive treatment is tumoral complete resection. An adequate approach and management requires comprehensive management from a multidisciplinary team involving among others, internists, cardiologists, urologists and nephrologists.
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