Giant Retroperitoneal Adrenal Ganglioneuroblastoma: Case Report
DOI:
https://doi.org/10.54212/27068048.v11i2.145Keywords:
Giant adrenal ganglioneuroblastomaAbstract
Introduction: Ganglioneuroblastoma is a rare tumor of the sympathetic nervous system, intermediate between malignant neuroblastoma and benign ganglioneuroma. It is common in children and rare in adults. Objective: To present the case of a patient diagnosed with adrenal ganglioneuroblastoma. Presentation of the case: A 45-year-old male patient, with no pathological history of interest. With a sensation of fullness associated with slight pain in the right hypochondrium. On positive physical examination in the abdomen, a single, slightly painful recurrent tumor was palpated, attached to deep planes that occupies the hypochondrium and the right flank, about 20 cm in diameter. No peritoneal reaction. Abdominal ultrasound showing a large complex retroperitoneal mass, suspecting a right adrenal tumor. Elements corroborated by contrasted CT. It was decided to intervene surgically and it was possible to enucleate the lesion that anatomically corresponds to the right adrenal gland. Satisfactory evolution. Paraffin biopsy concluded adrenal ganglioneuroblastoma. Conclusions: The relevance of this case is due to the fact that well-differentiated retroperitoneal ganglioneuroblastoma is a rare tumor in adults. The diagnosis of these tumors is based on the imaging study. In this case it was possible to resect the ganglioneuroblastoma in its entirety. The treatment is surgical
Downloads
References
Shimada H, Umehara S, Monobe Y, Hachitanda Y, Nakagawa A, Goto S, et al. International neuroblastoma pathology classification for pronostic evaluation of patients with peripheral neuroblastic tumors. Cancer. wiley [Internet].2001;92(9):2451-61. https://doi.org/10.1002/1097-0142(20011101)92:9<2451::AID-CNCR1595>3.0.CO;2-S DOI: https://doi.org/10.1002/1097-0142(20011101)92:9<2451::AID-CNCR1595>3.0.CO;2-S
Ganglioneuroblastoma de suprarrenales en un adulto. Informe de caso. cir ci . 2008;439-42.
. Fatimi SH, Bawany SA, Ashfaq A. Ganglioneuroblastoma of the posterior mediastinum: a case report. j med [Internet]. 2011;5(1):4. Disponible en: https://pdfs.semanticscholar.org/6bb9/cabf7ab90952dcc962b43eb2cc91863a51f5.pdf)
Jt. MWPR. Primary holocord ganglioneuroblastoma: Case report. J 0 Neurosurg Spine [Internet]. 2011;15(4):457-63. Disponible en:
https://doi.org/10.3171/2011.5.SPINE10563 DOI: https://doi.org/10.3171/2011.5.SPINE10563
Joshi VV, Rao PV, Cantor AB, Altshuler G, Shuster JJ, Castelberry RP. Modified histologic grading of neuroblastomas by replacement of mitotic rate with mitosis karyorrhexis index. A clinicopathologic study of 223 cases from the Pediatric Oncology Group. cancer. 1996;77(1):1582-8. https://doi.org/10.1002/(SICI)1097-0142(19960415)77:8<1582::AID-CNCR24>3.0.CO;2-V DOI: https://doi.org/10.1002/(SICI)1097-0142(19960415)77:8<1582::AID-CNCR24>3.0.CO;2-V
Corwin MT et al. , Adherence to guidelines for hormonal evaluation in patients with incidentally detected adrenal nodules: effects of radiology report wording and standardized reporting. abdo. 2020;45(9):2910-5. https://doi.org/10.1007/s00261-020-02517-3 DOI: https://doi.org/10.1007/s00261-020-02517-3
Santos M et al. Capítulo 34. En: Diretrizes Oncológicas 2a ed [Internet]. 2018. p. 557-62. Disponible en: https://diretrizesoncologicas.com.br/wp-content/uploads/2018/10/Diretrizes-oncol%C3%B3gicas-2_Parte34.pdf
Fujiwara T et al. . Results of Surgery for a Compound Adrenal Tomor Consisting of Pheochromocytoma and Ganglioneuroblastoma in an Adult. 5-year Follow-up. internal [Internet]. 2000;39(1):58-62. https://doi.org/10.2169/internalmedicine.39.58 DOI: https://doi.org/10.2169/internalmedicine.39.58
Downloads
Published
How to Cite
Issue
Section
License
Copyright (c) 2023 Deyanira Alexandra Tapia Inoa, Sonia Jiménez Reyes, Ariel Ramírez Pérez y Bashar Bassam Raja
This work is licensed under a Creative Commons Attribution 4.0 International License.
Authors who publish with this journal agree to the following terms:
- Authors retain copyright and grant the journal right of first publication with the work simultaneously licensed under a Creative Commons Attribution License 4.0 that allows others to share the work with an acknowledgement of the work's authorship and initial publication in this journal.
- Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.
- Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work.