Giant Retroperitoneal Adrenal Ganglioneuroblastoma: Case Report
DOI:
https://doi.org/10.54212/27068048.v11i2.145Keywords:
Giant adrenal ganglioneuroblastomaAbstract
Introduction: Ganglioneuroblastoma is a rare tumor of the sympathetic nervous system, intermediate between malignant neuroblastoma and benign ganglioneuroma. It is common in children and rare in adults. Objective: To present the case of a patient diagnosed with adrenal ganglioneuroblastoma. Presentation of the case: A 45-year-old male patient, with no pathological history of interest. With a sensation of fullness associated with slight pain in the right hypochondrium. On positive physical examination in the abdomen, a single, slightly painful recurrent tumor was palpated, attached to deep planes that occupies the hypochondrium and the right flank, about 20 cm in diameter. No peritoneal reaction. Abdominal ultrasound showing a large complex retroperitoneal mass, suspecting a right adrenal tumor. Elements corroborated by contrasted CT. It was decided to intervene surgically and it was possible to enucleate the lesion that anatomically corresponds to the right adrenal gland. Satisfactory evolution. Paraffin biopsy concluded adrenal ganglioneuroblastoma. Conclusions: The relevance of this case is due to the fact that well-differentiated retroperitoneal ganglioneuroblastoma is a rare tumor in adults. The diagnosis of these tumors is based on the imaging study. In this case it was possible to resect the ganglioneuroblastoma in its entirety. The treatment is surgical
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